Hemophagocytic syndrome associated with adult Still's disease
نویسندگان
چکیده
منابع مشابه
Childhood hemophagocytic syndrome associated with Kikuchi's disease.
Haematologica vol. 85(9):September 2000 was negative.The patient was treated with hydroxyurea, which decreased the size of his spleen and the number of peripheral eosinophils.A few months later he underwent an unrelated bone marrow transplantation and was in remission a year later. The diagnosis of CEL does not fit exactly the criteria proposed by Brito-Babapulle, since our patient has marked m...
متن کاملHemophagocytic syndrome associated with Kikuchi's disease.
A 13-yr-old female was admitted to our hospital with fever, seizure, and cervical lymphadenopathy. Laboratory data showed pancytopenia, elevation of serum transaminase, lactate dehydrogenase, triglyceride, and ferritin levels. Lymph node biopsy revealed features of Kikuchi's disease and there were signs of histiocytosis and hemophagocytic phenomenon in bone marrow. She recovered after treatment...
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Hemophagocytic lymphohistiocytosis (HLH) is a disease characterized by phagocytosis of blood cells by macrophages within the lymphoreticular tissue. It can develop secondary to some diseases or be familial as a result of genetic mutations. Niemann-Pick disease (NPD) is a very rare lipid storage disease. A three-month-old girl presented with high fever (39°C), abdominal distension and paleness. ...
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Adult-onset Still's disease (AOSD) is characterized by fever, rash, and joint pain and may lead to chronic arthritis. The cause of AOSD is unknown, and it is rare. We encountered a patient with adult-onset Still's disease following a sore throat and fever. The patient was a 40-year-old woman who consulted our hospital because of a sore throat, fever and arthritis. She was admitted and treated w...
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Reactive hemophagocytic syndrome (HPS) is characterized by hemophagocytosis by activated histiocytes, resulting in pancytopenia and liver dysfunction. We describe a patient with adult onset Still's disease (AOSD) in whom HPS developed. An 80-year-old Japanese woman with high fever, arthralgia, skin rash, and pleuritis was admitted to our hospital for further examination. She was diagnosed with ...
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ژورنال
عنوان ژورنال: RAED Dergisi
سال: 2016
ISSN: 1301-4021,2147-2548
DOI: 10.2399/raed.16.44127